Unusual presentation of a vascularized iris lesion in an infant Anilkumar SE, Shah PK, Saravanan V R, Shanthi R, Kalpana N, - J Indian Prosthodont Soc

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Unusual presentation of a vascularized iris lesion in an infant Sasikala Elizabeth Anilkumar¹, Parag K Shah², VR Saravanan³, Radhakrishnan Shanthi⁴, Narendran Kalpana¹ ¹ Department of Paediatric Ophthalmology and Strabismus, Aravind Eye Hospital and Postgraduate Institute of Ophthalmology, Coimbatore, Tamil Nadu, India ² Department of Paediatric Retina and Ocular Oncology, Aravind Eye Hospital and Postgraduate Institute of Ophthalmology, Coimbatore, Tamil Nadu, India ³ Department of Retina, Aravind Eye Hospital and Postgraduate Institute of Ophthalmology, Coimbatore, Tamil Nadu, India ⁴ Departments of Pathology, Aravind Eye Hospital and Postgraduate Institute of Ophthalmology, Madurai, Tamil Nadu, India Correspondence Address: Sasikala Elizabeth Anilkumar, Department of Paediatric Ophthalmology and Strabismus, Aravind Eye Hospital and Postgraduate Institute of Ophthalmology, Coimbatore - 641 014, Tamil Nadu India Source of Support: None, Conflict of Interest: None DOI: 10.4103/tjo.tjo_35_21

We report an unusual presentation of a 10-month-old girl with left eye (LE) redness and watering. Evaluation showed an iris vascular lesion and lens opacity in her LE. Child underwent USG B-scan and ultrasound biomicroscopy, by which an extensive mass lesion arising from iris and ciliary body with absent calcification was revealed. Following extensive evaluation, child underwent cataract extraction and trans-scleral total excision of the mass lesion. Histopathology proved it as juvenile xanthogranuloma (JXG) with vascular proliferation. JXG is a rare benign self-limiting dermatologic disorder affecting mainly infants and small children. Ocular lesions are the most common extracutaneous manifestation. Cataract in JXG is less frequently reported. This case is reported due to its rarity and as it presented solely as an intraocular lesion with combined diffuse infiltration into ciliary body and cataract which is unusual. Early recognition and systematic approach helped in sight saving and organ salvaging.

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    -  Anilkumar SE
    -  Shah PK
    -  Saravanan V R
    -  Shanthi R
    -  Kalpana N

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